| Item type |
学術雑誌論文 / Journal Article(1) |
| 公開日 |
2021-03-09 |
| タイトル |
|
|
タイトル |
Epidemiological Analysis of Major Complications Requiring Medical Intervention in Patients with Neurofibromatosis 1 |
|
言語 |
en |
| 言語 |
|
|
言語 |
eng |
| キーワード |
|
|
主題Scheme |
Other |
|
主題 |
neurofibromatosis 1 |
| キーワード |
|
|
主題Scheme |
Other |
|
主題 |
epidemiology |
| キーワード |
|
|
主題Scheme |
Other |
|
主題 |
treatment |
| キーワード |
|
|
主題Scheme |
Other |
|
主題 |
survey |
| キーワード |
|
|
言語 |
en |
|
主題Scheme |
Other |
|
主題 |
neurofibromatosis 1 |
| キーワード |
|
|
言語 |
en |
|
主題Scheme |
Other |
|
主題 |
epidemiology |
| キーワード |
|
|
言語 |
en |
|
主題Scheme |
Other |
|
主題 |
treatment |
| キーワード |
|
|
言語 |
en |
|
主題Scheme |
Other |
|
主題 |
survey |
| 資源タイプ |
|
|
資源タイプ |
journal article |
| 著者 |
吉田, 雄一
Ehara, Yuko
山元, 修
Ehara, Yuko
Koga, Monji
Imafuku, Shinichi
|
| 著者所属（英） |
|
|
言語 |
en |
|
値 |
Division of Dermatology, Department of Medicine of Sensory and Motor Organs, Faculty of Medicine, Tottori University |
| 著者所属（英） |
|
|
言語 |
en |
|
値 |
Division of Dermatology, Department of Medicine of Sensory and Motor Organs, School of Medicine, Tottori University Faculty of Medicine |
| 著者所属（英） |
|
|
言語 |
en |
|
値 |
Department of Dermatology, Fukuoka University School of Medicine |
| 著者所属（英） |
|
|
言語 |
en |
|
値 |
Department of Dermatology, Fukuoka University School of Medicine |
| 著者所属（英） |
|
|
言語 |
en |
|
値 |
Division of Dermatology, Department of Medicine of Sensory and Motor Organs, Faculty of Medicine, Tottori University |
| 抄録 |
|
|
内容記述タイプ |
Other |
|
内容記述 |
Neurofibromatosis 1 has various complications. To elucidate the frequency of neurofibromatosis 1-related major complications requiring medical intervention, a nationwide retrospective study was conducted of 3,530 patients with neurofibromatosis 1 registered from 2001 to 2014 in Japan. The ratio of certified patients requiring medical intervention (>stage 3) was 82%. Patients classified in the most severe grade experienced dermatological complications (71.8% of patients), neurological complications (38.1%) and bone complications (33.3%). In patients with dermatological manifestations, medical treatment was needed for cutaneous neurofibromas (58%), diffuse plexiform neurofibromas (31%) and malignant peripheral nerve sheath tumours (10%). Patients with neurological manifestations needed medical treatment mainly for brain tumours (53%) and intellectual disability (26%). Patients with bone manifestations needed medical treatment for pseudoarthrosis (9%), scoliosis (55%) and bone defects (16%). It is necessary for physicians to be aware of neurofibromatosis 1-related complications requiring medical intervention in order to provide appropriate care for patients with neurofibromatosis 1. |
| 書誌情報 |
ACTA DERMATO-VENEREOLOGICA
en : ACTA DERMATO-VENEREOLOGICA
巻 98,
号 8,
p. 753-756,
発行日 2018-09-15
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| 出版者 |
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|
出版者 |
ACTA DERMATO-VENEREOLOGICA |
| ISSN |
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|
収録物識別子タイプ |
ISSN |
|
収録物識別子 |
00015555 |
| 書誌レコードID |
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収録物識別子タイプ |
NCID |
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収録物識別子 |
AA00507245 |
| DOI |
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|
関連タイプ |
isIdenticalTo |
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|
識別子タイプ |
DOI |
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関連識別子 |
10.2340/00015555-2975 |
| 権利 |
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|
権利情報 |
This is an open access article under the CC BY-NC license. www.medicaljournals.se/acta Journal Compilation (C) 2018 Acta Dermato-Venereologica. |
| 情報源 |
|
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|
関連名称 |
Yoshida Yuichi, Ehara Yuko, Koga Monji, et al. Epidemiological Analysis of Major Complications Requiring Medical Intervention in Patients with Neurofibromatosis 1. ACTA DERMATO-VENEREOLOGICA. 2018. 98(8). 753-756. doi:10.2340/00015555-2975 |
| 関連サイト |
|
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|
識別子タイプ |
URI |
|
|
関連識別子 |
https://www.medicaljournals.se/acta/content/abstract/10.2340/00015555-2975 |
|
|
関連名称 |
https://www.medicaljournals.se/acta/content/abstract/10.2340/00015555-2975 |
| 著者版フラグ |
|
|
出版タイプ |
VoR |
| EISSN |
|
|
値 |
16512057 |
adv98(8)_753.pdf (390.8 kB)
